The web version contains additional material available at 10.1007/s42485-021-00060-3.A 16-year-old male presented with primary problem of worsening dorsal vertebral kyphoscoliosis (SKS) for three years. Now, he developed spasticity in legs, breathlessness on mild effort, and rest apneas. Aside from SKS, investigations unveiled rotatory atlantoaxial dislocation. Atlantoaxial fixation led to fast data recovery from all signs including from spinal deformity. Observations in this patient suggest that rotatory dislocation is a factor in spinal deformity.We present a report of two clients having the association of omovertebra, Sprengel’s deformity associated with the shoulder and Klippel-Feil abnormality with craniovertebral junctional uncertainty. Our literary works study did not find any report of these association. Importance of bone tissue alterations is reviewed. Two young clients served with neck discomfort, torticollis, webbed neck, and spastic quadriparesis. Both in patients, the investigations revealed basilar invagination, Klippel-Feil problem and Sprengel’s deformity associated with the shoulder. Apart from these fairly common associations, both the customers had omovertebral bone tissue that offered through the transverse process of C5 vertebra to scapula. Following atlantoaxial stabilization surgery, the patients quickly restored from all symptoms. Musculoskeletal abnormalities during the craniovertebral junction including Klippel-Feil abnormality, Sprengel’s neck, and omovertebra are secondary modifications to major atlantoaxial instability.A relatively unusual report of an 8-year-old girl with Maroteaux-Lamy syndrome this is certainly Type VI mucopolysaccharidosis who given apparent symptoms of spastic quadriparesis related to atlantoaxial uncertainty is presented. Atlantoaxial stabilization led to fast and sustained neurological recovery.Giant cellular reparative granuloma (GCRG) is a benign nonneoplastic granulomatous lesion and is rare within the cranial bone tissue. We present a pediatric case of the lesion as a result of the condyle and reduced clivus. A 9-year-old girl offered slowly progressive hoarseness and dysphagia. She showed left glossopharyngeal, vagus, and hypoglossal neurological palsy. An osteolytic lesion around the reduced clivus and condyle joint ended up being accompanied by deformation of the craniovertebral junction. An endoscopic endonasal approach had been utilized to decompress the cranial neurological and confirm the pathological finding. The lesion around the condyle was not resected to protect occipito-cervical security. The remainder lesion is seen carefully for a few months, and regrowth have not taken place. GCRG is a rare granulomatous lesion when you look at the cranial bone. This situation may be the first report of a pediatric clival GCRG. Treating pediatric GCRG is helpful.A spectrum of vertebral artery (VA) anomalies have been described with or without an associated congenital craniovertebral junction (CVJ) anomalies. C3 segmental VA, where the VA enters the dura at the level of C2/3 intervertebral foramen is an extremely uncommon anomaly. We report two cases of congenital CVJ anomaly (irreducible in one single with C2/3 fusion and reducible when you look at the other; without any subaxial fusion but with articular agenesis at C2/3 joint regarding the anomalous artery side). Calculated tomographic angiography revealed intraspinal intradural entry of VA through the C2/3 intervertebral foramen from the right side aided by the contralateral artery discovered crossing the atlanto-axial joint. Both the patients underwent posterior approach and C2 was spared from instrumentation both in instances. Postoperatively, the in-patient with irreducible dislocation restored well whilst the client with reducible dislocation expired, possibly additional into the thrombosis of the principal VA from C2/3 foraminal encroachment. C3 segmental VA might be advantageous in aggressively exposing the C1/2 joint but instrumentation of C2 or C3 needs caution in view of the likelihood of VA injury. Our knowledge demonstrates VA might be endangered even when revealing and protecting the artery. For such situations, we advice posterior decompression of the C2/3 neural foramen during instrumentation within the absence of connected C2/3 fusion, as an abnormal shared morphology of C2/3 shows a C2/3 instability.The incidence of intramedullary spinal cable metastasis (ISCM) has been increasing as the general success of patients with cancer tumors features improved by way of recent advanced therapies food as medicine , such as for example molecular targeted medications, anticancer representatives, and different irradiation practices. ISCM from lung and breast cancer is one of common kind among situations of ISCM. We report a very uncommon form of ISCM from gastric cancer. This 83-year-old man who’d a past health background of gastric adenocarcinoma given acute onset of paraparesis. Spinal magnetic resonance imaging unveiled an intramedullary lesion during the upper thoracic level. Due to quick worsening of his paresis, we chose to Biomass conversion perform tumefaction click here extirpation. Gross complete resection regarding the tumefaction ended up being successfully carried out. Pathological assessment revealed defectively differentiated adenocarcinoma, suggesting the diagnosis of ISCM from gastric cancer tumors. He demonstrated progressive enhancement of paraparesis immediately after surgery, although his overall survival had been limited by about half a year after surgery. Whenever examining the etiology of acute paraparesis in senior customers with a past medical background of disease, ISCM should be considered in the differential diagnosis.